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Fatal Familial Insomnia, A Prion Disease with a Mutation at Codon 178 of the Prion Protein Gene
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Fatal Familial Insomnia:Clinical and Pathologic Study of Five New Cases
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Clinicopathologic Conference, Genetic Creutzfeldt-Jakob Disease
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A 40-year old Woman with Difficulty Going Down Stairs in High-Heeled Shoes
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Wilson Disease: Description of 282 Patients Evaluated Over 3 Decades
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Fatal Familial Insomnia & Dysautonomia with Selective Degeneration of Thalamic Nuclei
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Movement Disorders in Patients with Genetic Developmental and Epileptic Encephalopathies
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Clinicopathologic Conference, Anti-IgLON5 IgG-Associated Neurologic Disorder
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A 77-Year-Old Man with Involuntary Movements, Sleep Changes, Falls, Bulbar Symptoms, and Cognitive Complaints
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Sporadic Creutzfeldt-Jakob Disease in a Very Young Person
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Antibody-Mediated Encephalitis
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IgLON5-mediated neurodegeneration is a differential diagnosis of CNS Whipple disease
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Intractable Epilepsy and Progressive Cognitive Decline in a Young Man
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A Case of Ataxia, Seizure, and Choreoathetosis in a 34-year-old Woman
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Choreoathetosis, Dystonia, and Myoclonus in 3 Siblings with Autosomal Recessive Spinocerebellar Ataxia Type 16
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Rapidly Progressive Quadriplegia and Encephalopathy
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A Variegated Squirrel Bornavirus Associated with Fatal Human Encephalitis
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A 27-Year Old Man with Rapidly Progressive Coma
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Anti-DPPX Encephalitis,Pathogenic Effects of Antibodies on Gut and Brain Neurons
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Enterovirus Vaccines for an Emerging Cause of Brain-Stem Encephalitis
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The Acquired Metabolic Disorders of the Nervous System, Uremic Encephalopathy
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Subacute Sclerosing Panencephalitis
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Viral Infections of the Nervous System, Chronic Meningitis, and Prior Diseases, Encephalitis Lethargica (non Economo Disease, sleeping sickness)
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Subacute Sclerosing Panencephalitis
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Clinical Reasoning: A 13-year-old Boy Presenting with Dystonia,Myoclonus,and Anxiety
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Clinicopathologic Conference, Kufs Disease (Autosomal Dominant) Parry Type Neuronal Ceroid Lypofuscinosis
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Diagnosing variant Creutzfeldt-Jakob disease: a retrospective analysis of the first 150 cases in the UK
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Progressive Encephalomyelitis with Rigidity and Myoclonus Gycine and NMDA Receptor Antibodies
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Treatment of Severe Neurological Deficits with IgG Depletion through Immunoadsorption in Patients with Escherichia coli O104:H4-Associated Haemolytic Uraemic Syndrome: A Prospective Trial
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Predictors of Neurologic Outcome in Hypothermia After Cardiac Arrest
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Subacute sclerosing panencephalitis: An Update
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CNS Lupus: A Study of 41 Patients
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Epilepsy Syndromes in Infancy
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The Serotonin Syndrome
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Clinicopath Conf, Prion Disease (Sporadic Creutzfeldt-Jakob Disease)
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A Practical Approach to the Diagnosis and Management of MELAS: Case Report and Review
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Subacute Sclerosing Panencephalitis
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Clinical Features of Nipah Virus Encephalitis Among Pig Farmers in Malaysia
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Serotonin Sydrome
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Fluid Attenuation Inversion Recovery (FLAIR) Images of Dentatorubropalliodoluysian Atrophy:Case Report
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Creutzfeldt-Jakob Disease and Related Transmissible Spongiform Encephalopathies
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Dentatorubral-Pallidoluysian Atrophy:Clin Features Closely Related to Unstable Expansion of Trinucleotide (CAG) Repeat
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The Relationship of Essential Tremor to Other Movement Disorders:Report on 678 Patients
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Familial Alzheimer's Disease
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Phenotype of Chromosome 14-Linked Familial Alzheimer's Disease in a Large Kindred
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